Prune Belly Syndrome: A Case Report and Literature Review

doi:10.12280/gjszjk.20230269

Abstract

Abstract:

We report a case in which prune belly syndrome (PBS) was detected by ultrasound examination at 13 weeks of gestation. The woman was pregnant for the first time and had no related genetic history in her family. No obvious abnormality was found by examination before 12 weeks of gestation. The fetal bladder was enlarged and protruded in the abdominal wall detected by ultrasound examination at 12 weeks of gestation. After 2 weeks, the fetal heart beat disappeared and the labor was induced. At present, the etiology and pathogenesis of PBS have not been specifically clarified. It is mostly considered that PBS could be caused by severe bladder outlet obstruction or mesoderm developmental defects secondary to 6 to 10 weeks of pregnancy. This case was analyzed and relevant literatures were reviewed in this paper. To discuss the etiology, pathogenesis, clinical manifestations and treatment of PBS will provide us more references for the clinical understanding, multidisciplinary management and individualized treatment of PBS.

Key words: Prune belly syndrome, Ultrasonography, prenatal, Prenatal diagnosis, Case reports

WANG Min, XU Fei-xue. Prune Belly Syndrome: A Case Report and Literature Review[J]. Journal of International Reproductive Health/Family Planning, 2024, 43(2): 111-114.

Figures/Tables 1

References 27

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