Abstract: Epithelioid trophoblastic tumor (ETT) is a rare gestational trophoblastic neoplasia (GTN), accounting for 1.39%-2% of GTN. ETT occurs mostly in women of childbearing age, especially after full-term pregnancy. The clinical manifestations are of nontypical, and the definite diagnosis is mainly based on the histopathologic examination. Surgery is the preferred option for the treatment of ETT，and the effect of chemotherapy and local radiotherapy remains controversial and individual. The factors of ETT prognosis are ambiguous, including the extra-uterinelesion  the interval over 4 years from the antecedent pregnancy. The prognosis could be better in patients without metastasis，but very poor in those patients with metastasis.

Key words: Trophoblastic neoplasms；, Diagnosis；, Therapy；, Prognosis；, Case reports