Abstract:

Dermatofibrosarcoma protuberans (DFSP) is a rare dermal stromal tumor, and DFSP occurring in the vulva is even rarer in clinical practice. Pathological examination combined with immunohistochemical staining is the main method of diagnosis, and surgery is usually the main treatment. We reported a case of vulvar DFSP. After resection of vulvar mass in a local hospital, the postoperative examination indicated DFSP, so the patient was transferred to our hospital for the supplementary treatment. After surgical resection, the residual lesion was examined for pathology and immunohistochemistry. The diagnosis of vulva DFSP was confirmed again, and the supplementary chemotherapy was given after surgery. By discussing the etiology, pathogenesis, clinical manifestations, pathological types, diagnosis and differential diagnosis, treatment, prognosis and follow-up of the disease, we can deepen the understanding of this disease.

Key words: Vulvar neoplasms, Dermatofibrosarcoma, Diagnosis, Therapy, Prognosis, Case reports