类似卵巢性索肿瘤的子宫肿瘤合并子宫腺肌病一例

doi:10.12280/gjszjk.20250071

摘要/Abstract

摘要：

类似卵巢性索肿瘤的子宫肿瘤（uterine tumor resembling ovarian sex cord tumor，UTROSCT）作为一种特殊病理类型的子宫原发肿瘤，因临床上极为罕见，且无特殊临床表现，导致早期诊断困难。报告1例UTROSCT合并子宫腺肌病病例，患者因发现子宫肌瘤3个月余，阴道间断性出血12 d入院，门诊以子宫肌瘤收治入院，入院后完善相关辅助检查，盆腔超声提示子宫肌瘤可能，肿瘤标志物等未见明显异常。行单孔腹腔镜下子宫肌瘤剔除术+机会性输卵管切除，术中见瘤体包膜为灰白色，瘤体极软，瘤体与子宫界限不清，术中快速病理检查提示小细胞恶性肿瘤可能，遂立即行全子宫+双侧附件切除术，最终术后病理回报为UTROSCT。术后随访4年，患者病情稳定，未见复发。手术治疗是UTROSCT的主要治疗手段，预后通常良好，但需注意复发和转移的可能性。

关键词: 子宫肿瘤, 卵巢, 子宫腺肌病, 超声检查, 免疫组织化学

Abstract:

The uterine tumor resembling ovarian sex cord tumor (UTROSCT), as a special pathological type of primary uterine tumor, is difficult to be diagnosed early due to its extreme rarity and unspecial manifestations in clinical. We report a case of UTROSCT combined with adenomyosis. The patient was admitted to the hospital due to the discovery of uterine fibroids for more than 3 months and intermittent vaginal bleeding for 12 days. The patient was admitted the hospital with a outpatient diagnosis of uterine fibroids. After admission, the relevant auxiliary examinations were completed. Pelvic ultrasound suggested the possibility of uterine fibroids, and there was no obvious abnormalities in tumor markers. Single-port laparoscopic myomectomy and opportunistic salpingectomy were performed. During the operation, the tumor capsule was gray-white, the tumor was extremely soft, and the boundary between the tumor and the uterus was unclear. The intraoperative rapid pathological examination suggested the possibility of small-cell malignant tumor, so total hysterectomy and bilateral adnexectomy were immediately performed. Finally, the postoperative pathology report showed UTROSCT. After 4-year follow-up, the patient′s condition was stable and there was no recurrence. We concluded that surgical treatment is the main treatment for UTROSCT, the prognosis is usually good, and that the possibility of recurrence and metastasis should be noted.

Key words: Uterine neoplasms, Ovary, Adenomyosis, Ultrasonography, Immunohistochemistry

柴玲娜, 石洁, 李艳丽, 高晗, 程诗语, 欧阳夕颜. 类似卵巢性索肿瘤的子宫肿瘤合并子宫腺肌病一例[J]. 国际生殖健康/计划生育杂志, 2025, 44(5): 383-387.

CHAI Ling-na, SHI Jie, LI Yan-li, GAO Han, CHENG Shi-yu, OUYANG Xi-yan. A Case of Uterine Tumor Resembling Ovarian Sex Cord Tumor with Adenomyosis[J]. Journal of International Reproductive Health/Family Planning, 2025, 44(5): 383-387.

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